摘要：

There are several pathophysiological processes in the cases of pulmonary hypertension in patients with sarcoidosis. Pulmonary fibrosis causes pulmonary hypertension by reducing vascular beds. A few reports identified a possibility of veno-occlusive lesions as the cause of pulmonary hypertension in patients with sarcoidosis. Oppression due to lymphadenopathy may cause pulmonary hypertension which can be treated by corticosteroids. Although its recognition seems to be not yet widespread, the presence of pulmonary hypertension is a factor contributing to the intractability of sarcoidosis. Here, we try to review the backgrounds, frequency, diagnostic approach, and therapeutic topics.

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