Multiple Cystic Lung Diseases
摘要：
Multiple cystic lung disease (MCLD) is a rare condition consisting of multiple, usually round, parenchymal lucencies of low-attenuating area with wall thickness less than 2 mm. The most characteristic clinical feature is pneumothorax, and diffuse cysts may lead to respiratory failure. Lymphangioleiomyomatosis, Langerhans cell histiocytosis, and folliculin (FLCN) syndrome (Birt-Hogg-Dubé) represent the "big three" MCLD. Other causes comprise Sjgren syndrome and other lymphoid disorders, infections, malignancies, etc. The multiple cystic lung diseases (MCLD) have been increasingly recognised after high resolution computed tomography (HRCT) became available. They are typically rare and orphan conditions which encompass a large spectrum of aetiologies.
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关键词：
Lung cysts Lymphangioleiomyomatosis – Birt-Hogg-Dubé syndrome FLCN syndrome – Langerhans cell histiocytosis Sjögren syndrome Immunoglobulin deposition disease
DOI：
10.1007/978-1-4471-2401-6_16
被引量：
年份：
2015
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